Issue 4-98, 2020

Original article

https://doi.org/10.38025/2078-1962-2020-98-4-4-13

Compensatory Strategies in Children with Upper Limbs Deformities due to Amioplasia

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1 ORCIDAgranovich O.E., 1 ORCIDSavina M.V., 1,2 ORCIDOreshkov A.B., 1,3 ORCIDBlagoveshchensky E.D.

1 Turner Scientific research institute for children’s orthopedics, Saint-Petersburg, Russian Federation
2 Saint-Petersburg Institute of Postgraduate Medical experts, Saint-Petersburg, Russian Federation
3 National Research University «Higher School of Economics», Moscow, Russian Federation


ABSTRACT

Amyoplasia is the most severe form of arthrogryposis and is characterized by congenital multiple joint contractures,hypoplasia or aplasia of skeletal muscles, and limited or complete lack of self-service. The use of compensatory movementsallows patients to be partially or completely independent in daily life.The goal. Based on their own observations and literature, describe compensatory and compensatory movements in childrenwith amyoplasia with upper limb lesions, which patients use in performing basic self-care skills.Material and methods. From 2008 to 2019 we examined, 236 patients with amyoplasia (10 months to 16 years old) with atypical lesion of the upper extremities and limitation of self-care. Depending on the nature of the existing anatomical andfunctional disorders and the level of segmental muscle damage, all patients with amyoplasia were divided into 4 groups.Compensatory movements were studied in each group of patients.results. The study showed that children's compensatory movements are numerous and depend on the degree of musclefunction disorders of the upper and lower extremities, the rate of psychomotor development of the child. Elbow is a key jointto determine the functional independence in daily life. In cases of extensor contracture in the elbow patients have severefunctional disorders and need personal assistance.Conclusions. Compensatory movements in children with amyoplasia are useful and help to adapt in daily life andcompensate for the loss (or insufficiency) of movements in the joints. Compensatory movements in children are different.they are determined by the range of passive and active movements in the joints of the upper and low extremities.


KEYWORDS: arthrogryposis, amyoplasia, contractures, compensatory strategies, muscles, daily activity

FOR CITATION: Agranovich O.E., Savina M.V., Oreshkov A.B., Blagoveshchensky E.D. Compensatory Strategies in Children with Upper Limbs Deformities due to Amioplasia. Bulletin of Rehabilitation Medicine. 2020; 4 (98): 4–13. https://doi.org/10.38025/2078–1962–2020–98–4–4–13


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This is an open article under the CC BY 4.0 license. Published by the National Medical Research Center for Rehabilitation and Balneology.